rspНаучно-практическая ревматологияRheumatology Science and Practice1995-44841995-4492IMA-PRESS, LLC10.47360/1995-4484-2024-653-659rsp-3663Research ArticleКЛИНИЧЕСКИЙ СЛУЧАЙCLINICAL OBSERVATIONЭнхондроматоз (болезнь Оллье): обзор литературы и описание клинического случаяEnchondromatosis (Ollier’s disease): literature review and clinical case descriptionhttps://orcid.org/0000-0002-6064-7880ДенисовЛ. Н.DenisovL. N.

Денисов Лев Николаевич 

115522, Москва, Каширское шоссе, 34а

Lev N. Denisov 

115522, Moscow, Kashirskoye Highway, 34A

lev-denisov1941@mail.ruhttps://orcid.org/0000-0001-7418-9369СмирновА. В.SmirnovA. V.

115522, Москва, Каширское шоссе, 34а

Alexander V. Smirnov 

115522, Moscow, Kashirskoye Highway, 34A

https://orcid.org/0000-0002-7179-8174НестеренкоВ. А.NesterenkoV. A.

115522, Москва, Каширское шоссе, 34а

Vadim A. Nesterenko 

115522, Moscow, Kashirskoye Highway, 34A

ФГБНУ «Научно-исследовательский институт ревматологии им. В.А. Насоновой»РоссияV.A. Nasonova Research Institute of RheumatologyRussian Federation202427122024626653659Copyright © Денисов Л.Н., Смирнов А.В., Нестеренко В.А., 20242024Денисов Л.Н., Смирнов А.В., Нестеренко В.А.Denisov L.N., Smirnov A.V., Nesterenko V.A.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://rsp.mediar-press.net/rsp/article/view/3663

Болезнь Оллье (энхондроматоз, дисхондроплазия) – это нарушение роста и развития костной структуры, проявляющееся образованием очагов хрящевой ткани в одной или нескольких костях скелета. Сопровождается деформацией, укорочением и нарушением функции вовлеченных в патологический процесс сегментов костного аппарата. Энхондроматоз является редким заболеванием. В конце XX века в специализированной литературе было упомянуто о 30 случаях болезни. Учитывая недостаточное знакомство врачей с данной патологией, обусловливающее трудности в диагностике, представлен обзор литературы и описание клинического случая.

Ollier’s disease (enchondromatosis, dyschondroplasia) is a violation of the growth and development of bone structure, manifested by the formation of foci of cartilage tissue in one or more bones of the skeleton. It is accompanied by deformation, shortening and dysfunction of the segments of the bone apparatus involved in the pathological process. Enchondromatosis is a rare disease. At the end of the 20th century, 30 cases of the disease were mentioned in the specialized literature. Taking into account the insufficient familiarity of doctors with this pathology, which causes difficulties in diagnosis, a review of the literature and a description of the clinical case are presented.

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The authors declare that there are no conflicts of interest present.