Легочная артериальная гипертензия при системных заболеваниях соединительной ткани
https://doi.org/10.14412/1995-4484-2015-69-77
Аннотация
В лекции рассматривается проблема одного из редких проявлений системных заболеваний – легочной артериальной гипертензии. Указывается необходимость ранней диагностики, тщательной дифференциальной диагностики, верификации диагноза с применением инвазивных способов оценки центральной гемодинамики. Представлена модель скрининга больных с системной склеродермией, упрощающая определение показаний для назначения методов, позволяющих верифицировать диагноз. Описаны современные подходы к лекарственной терапии, обсуждаются вопросы улучшения выживаемости пациентов с этой прогностически неблагоприятной патологией.
Об авторе
А. В. ВолковРоссия
заведующий лабораторией инструментальной диагностики ФГБНУ НИИР им. В.А. Насоновой, канд. мед. наук
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Рецензия
Для цитирования:
Волков А.В. Легочная артериальная гипертензия при системных заболеваниях соединительной ткани. Научно-практическая ревматология. 2015;53(1):69-77. https://doi.org/10.14412/1995-4484-2015-69-77
For citation:
Volkov A.V. PULMONARY ARTERIAL HYPERTENSION IN CONNECTIVE TISSUE DISEASES. Rheumatology Science and Practice. 2015;53(1):69-77. (In Russ.) https://doi.org/10.14412/1995-4484-2015-69-77