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THE USE OF TUMOR NECROSIS FACTOR α INHIBITORS IN PATIENTS WITH WEBER-CHRISTIAN DISEASE

https://doi.org/10.14412/1995-4484-2013-721-4

Abstract

Weber-Christian disease (WCD), also known as idiopathic lobular panniculitis, is a rare disease belonging to the group of diffuse connective tissue diseases. No therapy for WCD has been developed; empirical treatment is typically used. The first description of the use of tumor necrosis factor α inhibitors in a female patient with infiltrative WCD is presented. The tactics of managing this patient category are analyzed.

About the Authors

Olga Nikolayevna Egorova
Nasonova Research Institute of Rheumatology, Russian Academy of Medical Sciences, Moscow, Russia
Russian Federation


B S Belov
Nasonova Research Institute of Rheumatology, Russian Academy of Medical Sciences, Moscow, Russia
Russian Federation


S G RadenskaLopovok
Nasonova Research Institute of Rheumatology, Russian Academy of Medical Sciences, Moscow, Russia
Russian Federation


O V Pushkova
Nasonova Research Institute of Rheumatology, Russian Academy of Medical Sciences, Moscow, Russia
Russian Federation


N M Savushkina
Nasonova Research Institute of Rheumatology, Russian Academy of Medical Sciences, Moscow, Russia
Russian Federation


Ya B Khrennikov
Nasonova Research Institute of Rheumatology, Russian Academy of Medical Sciences, Moscow, Russia
Russian Federation


E L Nasonov
Nasonova Research Institute of Rheumatology, Russian Academy of Medical Sciences, Moscow, Russia
Russian Federation


Review

For citations:


Egorova O.N., Belov B.S., RadenskaLopovok S.G., Pushkova O.V., Savushkina N.M., Khrennikov Ya.B., Nasonov E.L. THE USE OF TUMOR NECROSIS FACTOR α INHIBITORS IN PATIENTS WITH WEBER-CHRISTIAN DISEASE. Rheumatology Science and Practice. 2013;51(6):721-4. (In Russ.) https://doi.org/10.14412/1995-4484-2013-721-4

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ISSN 1995-4484 (Print)
ISSN 1995-4492 (Online)