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Review of guideline for the management of ANCA-associated vasculitis, presented in 2021 by the American College of Rheumatology/Vasculitis Foundation

https://doi.org/10.47360/1995-4484-2021-684-692

Abstract

The anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitides (AAVs) are a group of severe life-threatening autoimmune diseases, and one of the most important problems in practical rheumatology. This article discusses 2021 American College of Rheumatology/Vasculitis Foundation guideline for the management of AAVs, including granulomatosis with polyangiitis (GPA), microscopic polyangiitis (MPA), and eosinophilic granulomatosis with polyangiitis (EGPA). The guideline features 26 recommendations and 5 upgraded position statements for GPA/ MPA, as well as 15 recommendations and 5 upgraded position statements for EGPA, which became the basis for the proposed algorithms for the treatment of patients with GPA/MPA and EGPA. Particular attention has been paid to the use of biologics.

About the Authors

T. V. Beketova
V.A. Nasonova Research Institute of Rheumatology; Central Clinical Hospital of the Administrative Directorate of the President of the Russian Federation
Russian Federation

Tatiana V. Beketova.

115522, Moscow, Kashirskoye Highway, 34A; 121359, Moscow, Marshala Timoshenko str., 15.


Competing Interests:

No



I. Yu. Popov
V.A. Nasonova Research Institute of Rheumatology
Russian Federation

Ivan Yu. Popov.

115522, Moscow, Kashirskoye Highway, 34A.


Competing Interests:

No



V. V. Babak
V.A. Nasonova Research Institute of Rheumatology
Russian Federation

Valeriya V. Babak.

115522, Moscow, Kashirskoye Highway, 34A.


Competing Interests:

No



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Review

For citations:


Beketova T.V., Popov I.Yu., Babak V.V. Review of guideline for the management of ANCA-associated vasculitis, presented in 2021 by the American College of Rheumatology/Vasculitis Foundation. Rheumatology Science and Practice. 2021;59(6):684-692. (In Russ.) https://doi.org/10.47360/1995-4484-2021-684-692

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ISSN 1995-4484 (Print)
ISSN 1995-4492 (Online)